Familial Multiple Endocrine Neoplasia Type 1-associated Pulmonary Typical Carcinoid and Thymic Atypical Carcinoid—Report of a Surgical Case—
نویسندگان
چکیده
منابع مشابه
Thymic carcinoid associated with multiple endocrine neoplasia syndrome type I.
Thymic carcinoids are a rare entity that may be associated with endocrine diseases like Cushing's syndrome or multiple endocrine neoplasia syndrome type I (MEN1). These tumors represent 4% of anterior mediastinal tumors and are characterized by their very aggressive behavior. We present the case of a patient with a previous MEN 1 diagnosis in whom, during the follow up of his disease, a thoraci...
متن کاملCoexisting Thymic and Pulmonary Carcinoid Tumors Associated with Multiple Endocrine Neoplasia Type1.
An anterior mediastinal tumor was detected in a 45-year-old female during a medical checkup. Chest computed tomography (CT) showed the anterior mediastinal tumor and a pulmonary tumor in the right lower lobe. Furthermore, tumors of the parathyroid gland, pancreas, and pituitary gland were also detected. She was clinically diagnosed with multiple endocrine neoplasia type1 (MEN1). The patient und...
متن کامل[Bronchial carcinoid and type 1 multiple endocrine neoplasia syndrome. A case report].
Carcinoid tumours of bronchial origin are rare in type 1 multiple endocrine neoplasia (MEN1) syndrome. The prevalence of histologically confirmed cases is approximately 5-8%, although in more recent studies it is estimated that it could be much higher and a possible relationship with the presence of hypergastrinaemia is suggested. We report a patient with a type 1 MEN syndrome, with no respirat...
متن کاملAtypical clinical manifestations of multiple endocrine neoplasia type 1 syndrome.
Multiple endocrine neoplasia type 1 (MEN1) is a hereditary tumor syndrome characterized by a genetic predisposition to develop a variety of neuroendocrine tumors and hormone excess syndromes. The major components of MEN1 are hyperparathyroidism due to multiple parathyroid adenomas or hyperplasia, duodenopancreatic neuroendocrine tumors and pituitary adenomas, most often producing prolactin. Phy...
متن کاملThymic carcinoid in the setting of a multiple endocrine neoplasia syndrome (MEN 1). Prophylactic thymectomy?
ar enlargement, and no other signs of sexual development; ome mechanisms proposed for this phenomenon impliate the NR0B1 gene in the prepubertal control mechanism f the gonadal axis, ACTH-mediated stimulus of testicuar steroidogenesis, or autonomous hyperplasia of Leydig ells.2 In the pubertal period, these patients will require estosterone replacement for the development of secndary sexual cha...
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ژورنال
عنوان ژورنال: Nihon Rinsho Geka Gakkai Zasshi (Journal of Japan Surgical Association)
سال: 2019
ISSN: 1345-2843,1882-5133
DOI: 10.3919/jjsa.80.1831